Kawasaki Disease (Mucocutaneous Lymph Node Syndrome)
Kawasaki Disease (Mucocutaneous Lymph Node Syndrome) Sarah D. de Ferranti Jane C. Burns Jane W. Newburger Kawasaki disease (KD), first described in Japan in 1967 by Dr. Kawasaki, is now…
Pulmonary Atresia and Intact Ventricular Septum
Pulmonary Atresia and Intact Ventricular Septum David G. Nykanen Robert Mark Freedom 1941–2005 A discussion of pulmonary atresia and intact ventricular septum would be incomplete without acknowledging the legacy of…
Double-Outlet Right Ventricle
Double-Outlet Right Ventricle Gail E. Wright Katsuhide Maeda Norman H. Silverman Frank L. Hanley Stephen J. Roth Definition Double-outlet right ventricle (DORV) is a type of ventriculoarterial connection in which…
Aortic Arch and Vascular Anomalies
Aortic Arch and Vascular Anomalies David S. Ezon Daniel J. Penny Introduction It can be challenging to develop an adequate understanding of the three-dimensional interrelationships of the thoracic vessels and…
Aortic Stenosis
Aortic Stenosis Joshua M. Friedland-Little Jeffrey D. Zampi Robert J. Gajarski Introduction Congenital obstruction of the left ventricular outflow tract comprises a heterogeneous group of disorders, with obstruction potentially occurring…
Abnormal Systemic Venous Connections
Abnormal Systemic Venous Connections Tal Geva The word vein stems from the Latin vena (from the Latin verb venio, “to come”). Hence, a vein is a passage, a conduit, a…
Anomalies of the Pulmonary Veins
Anomalies of the Pulmonary Veins David W. Brown Tal Geva Anomalies of the pulmonary veins vary widely in their anatomic spectrum and clinical presentation, course, and outcome. As with other…
Tetralogy of Fallot with Pulmonary Stenosis, Pulmonary Atresia, and Absent Pulmonary Valve
Tetralogy of Fallot with Pulmonary Stenosis, Pulmonary Atresia, and Absent Pulmonary Valve S. Lucy Roche Steven C. Greenway Andrew N. Redington Tetralogy of Fallot (TOF) is a spectrum of diseases,…
Vascular Tumors and Anomalies
Vascular Tumors and Anomalies Ahmad I. Alomari Introduction Vascular anomalies are relatively common heterogenous disorders characterized by developmentally abnormal blood vessels including the venous, arterial, and lymphatic lineages. These anomalies…
Truncus Arteriosus
Truncus Arteriosus Allison K. Cabalka William D. Edwards Joseph A. Dearani Persistent truncus arteriosus is an uncommon congenital cardiovascular malformation. There is no striking gender difference in frequency, although most…
