Abstract Heart failure in children occurs with a heterogenous group of congenital and acquired diseases. Systolic ventricular dysfunction is the most common cause of pediatric heart failure; however, primary diastolic…
Abstract Atrial septal defects (ASDs) are a group of anatomic abnormalities that result in shunting of blood between the atria. ASD is the second most common congenital heart lesion after…
Abstract Pulmonary hypertension is a formidable challenge to the care of children with congenital heart disease, with a burgeoning incidence in the perioperative period. Awareness of this problem, prospective clinical…
Abstract The goal of staged reconstructive surgery for children with single-ventricle defects is ultimately to achieve a modified Fontan circulation. The modified Fontan circuit allows systemic venous blood from both…
Abstract The field of human genetics has achieved dramatic growth since the publication of the second edition of this textbook. The capabilities of genetic testing technology to interrogate the genome…
Abstract This chapter provides an overview of the topic of tetralogy of Fallot with and without pulmonary atresia, covering areas from history and genetics to current management issues and methods,…
Abstract: Biventricular repair requires two ventricles, each capable of supporting the systemic and pulmonary circulation. Septation has been interpreted as the pursuit of biventricular circulation rather than single-ventricle track. Although…
Abstract Double-outlet right ventricle (DORV) describes a ventriculoarterial connection in which both great arteries associate primarily with the right ventricle in an array of possible arrangements that can produce physiologies…
Abstract This chapter describes the disease spectrum of pulmonary atresia with intact ventricular septum (PA/IVS). It reviews the embryology, anatomy, physiology, treatment algorithms, and surgical techniques and outcomes. PA/IVS is…
Abstract Isomerism is a unique clinical entity in which there is duplication of one half of the body across the vertical axis, leading to a loss of laterality in the…
