Pulmonary Sarcoidosis Allen P. Burke, M.D. Marie-Christine Aubry, M.D. Seth Kligerman, M.D. Definition Sarcoidosis is a systemic disease characterized histologically by the presence of nonnecrotizing granulomas, with lung involvement occurring…
Acute Respiratory Distress Syndrome Marie-Christine Aubry, M.D. Allen P. Burke, M.D. Definition Acute respiratory distress syndrome (ARDS) is defined clinically and is, as such, not a pathologic term. Until recently,…
Rare Idiopathic Interstitial Pneumonias Allen P. Burke, M.D. Marie-Christine Aubry, M.D. Seth Kligerman, M.D. Idiopathic Pleuroparenchymal Fibroelastosis Background Idiopathic pleuroparenchymal fibroelastosis (PPFE) was initially described in 2004 as a form…
Acute and Subacute Idiopathic Interstitial Pneumonias Marie-Christine Aubry, M.D. Allen P. Burke, M.D. Seth Kligerman, M.D. Cryptogenic Organizing Pneumonia Terminology One of the first uses of a term related to…
Smoking-Related Idiopathic Interstitial Pneumonias Allen P. Burke, M.D. Fabio R. Tavora, M.D., Ph.D. Seth Kligerman, M.D. Marie-Christine Aubry, M.D. Respiratory Bronchiolitis—Interstitial Lung Disease Terminology Respiratory bronchiolitis (RB) and desquamative interstitial…
Chronic Fibrosing Idiopathic Interstitial Pneumonias Marie-Christine Aubry, M.D. Allen P. Burke, M.D. Seth Kligerman, M.D. Usual Interstitial Pneumonia/Idiopathic Pulmonary Fibrosis Terminology Usual interstitial pneumonia (UIP) is a form of diffuse…
Diffuse Parenchymal Lung Disease: Classification and Concepts Marie-Christine Aubry, M.D. Allen P. Burke, M.D. Terminology Diffuse parenchymal lung disease (DPLD), also known as interstitial lung disease, encompasses a broad heterogeneous…
Pediatric Interstitial Lung Disease and Hermansky-Pudlak Syndrome Allen P. Burke, M.D. Jennifer M. Boland, M.D. Pediatric Interstitial Lung Disease Terminology and Classification Children’s interstitial lung disease (ChILD) can generally be…
Congenital Pulmonary Vascular Disease Allen P. Burke, M.D. Jennifer M. Boland, M.D. Persistent Pulmonary Hypertension of the Newborn Etiology and Clinical Findings Persistent pulmonary hypertension of the newborn (PPHN) is…
Lung Disease in Premature Infants Thais Mauad, M.D., Ph.D. Jennifer M. Boland, M.D. Background One out of every nine live births in the United States and Europe occurs at <37…
