Marfan syndrome is an autosomal dominant disorder of connective tissue in which cardiovascular, skeletal, and ocular abnormalities may be present to a highly variable degree. Prevalence has been estimated at…
The clinical presentation of constrictive pericarditis is similar to that of restrictive cardiomyopathy: predominantly signs of systemic venous congestion and less pronounced signs of low cardiac output. The distinction between…
Anomalous coronary arteries are frequently seen in conjunction with certain other congenital cardiac defects and may even be considered inherent in some anomalies, such as in transposition of the great…
Until the second half of the past century, cardiac tumors were diagnosed almost exclusively at autopsy. However, advances in cardiac imaging and the development of cardiopulmonary bypass made cardiac tumors…
Idiopathic pulmonary arterial hypertension (IPAH) is a rare progressive disease that eventually, if left untreated, progresses to right heart failure and death. The first pathologic description of the condition dates…
Definition Hypertrophic cardiomyopathy (HCM) is defined as left ventricular (LV) hypertrophy in the absence of abnormal loading conditions (valve disease, hypertension, congenital heart defects) sufficient to explain the degree of…
Rheumatic fever (RF) is an inflammatory disease that affects various systems such as the skin, brain, cardiovascular system, and many mucosal membranes, that is, the pericardium, the pleura and the…
Definitions Noncompacted myocardium (NCM) is a cardiac abnormality involving the myocardial wall, characterized by numerous, excessively prominent trabeculations and deep intertrabecular recesses penetrating into the midmyocardium ( Fig. 64.1 )….
Acknowledgments This work has been supported by TRANSAC, University of Padua Strategic Project CPDA133979/13, Padua, Italy; Registry for Cardio-cerebro-vascular Pathology, Veneto Region, Venice, Italy; Target Project, Regional Health System, Venice,…
The cardiomyopathies represent an important group of heart muscle disorders that are all associated with significant morbidity and mortality. The most prevalent of these conditions is dilated cardiomyopathy (DCM), which…
