Summary Malignant ventricular arrhythmias and sudden cardiac death may late happen in repaired tetralogy of Fallot, although probably less frequently than previously thought, especially with the advent of new surgical…
Summary With the advances in congenital cardiac surgery and postoperative care, an increasing number of children with complex congenital heart disease now reach adulthood. There are already more adults than…
Summary Supraventricular arrhythmias are an important and increasing cause of morbidity in adults with congenital heart disease, requiring specific management strategies. Pharmacological treatment has limited efficacy, and is often associated…
Summary Background Ebstein’s anomaly is a complex malformation. Justification of a procedure in mildly symptomatic adults is debatable: repair techniques are demanding and valve replacement is associated with poorer outcome….
Summary Background Adolescents and young adults with congenital heart disease (CHD) have complex health needs and require lifelong follow-up. Interventions to facilitate the paediatric-to-adult healthcare transition are recommended, but outcomes…
Summary Background The relationship between pulmonary arterial hypertension-specific drug therapy (PAH-SDT) and mortality in Eisenmenger syndrome (ES) is controversial. Aims To investigate outcomes in patients with ES, and their relationship…
Summary Background Monomorphic ventricular tachycardia (MVT) is common in adults with repaired tetralogy of Fallot (TOF), and is associated with sudden cardiac death. Management of MVT is not defined, and…
Summary Background Heart failure (HF) is the main cause of death in adult congenital heart disease (ACHD). Aims We aimed to characterize HF-related hospitalization of patients with ACHD, and to…
Advances in medical and surgical care have produced remarkable improvements in the survival of children with congenital heart disease (CHD); around 90% of children with CHD now reach adulthood ….
Owing to improvements in the management of congenital heart disease (CHD), the number of adults living with a diagnosed, repaired or palliated CHD is increasing constantly. The specificity and the…
