Tetralogy of Fallot
The anomaly now known as the tetralogy of Fallot (TOF) was first described, insofar as is known, by Niels Stensen in 1671. He was also known in Latin as Nicolaus…
CARDIOLOGY
Pulmonary Venous Anomalies
Totally Anomalous Pulmonary Venous Connection/Drainage Definition Totally anomalous pulmonary venous connection (TAPVC) is an anomaly in which none of the pulmonary veins connect normally with the morphologically left atrium (LA)….
Common Atrioventricular Canal
Acknowledgment I would like to thank Silvio Litovsky, M.D., for his great help in analyzing the data on which this chapter is based. Definition The anomaly known as common atrioventricular…
Interatrial Communications
How common are interatrial communications —mostly the theostium secundum type of atrial septal defect and ostium primum type of atrial septal defect ( Figs. 9.1 and 9.2 )? Is atrial…
Juxtaposition of the Atrial Appendages
The anomaly now known as juxtaposition of the atrial appendages (JAA) was first described, to the best of our knowledge, by Thore in 1843 in an 11-day-old boy with left-sided…
Double-Outlet and Common-Outlet Right Atrium
Definition The morphologically right atrium (RA) opens into both the morphologically right ventricle (RV) and the morphologically left ventricle (LV) via two atrioventricular (AV) valves resulting in double-outlet right atrium…
Cor Triatriatum Sinistrum (Subdivided Left Atrium) and Cor Triatriatum Dextrum (Subdivided Right Atrium)
Definition The classic form of cor triatriatum (meaning “heart with three atria”) may be defined as a rare cardiac malformation in which the left atrium (LA) is subdivided into dorsal…
Systemic Venous Anomalies
We shall begin the specific anomalies section with systemic venous malformations because this book is organized in a venoarterial or blood-flow sequence—segment by segment, alignment by alignment, and connection by…
Segmental Anatomy
The segmental approach to the diagnosis of congenital heart disease is based on an understanding of the morphologic and segmental anatomy of the heart. The morphologic anatomy of the heart…
The Congenital Cardiac Pathology Database
An accurate, statistically analyzed database is considered to be of fundamental importance in the effort to make our field more quantitative. At present, almost no book on pediatric cardiology, pediatric…
