What are the outcomes that really matter to patients, families, and societies living with the implications of congenital and acquired paediatric cardiac disease? Survival and physiological function are certainly paramount….
Kawasaki disease was first described in 1967, by a Japanese paediatrician, Tomisako Kawasaki. 1 He characterised the illness, then termed mucutaneous lymph node syndrome, as including high fever, non-exudative conjunctivitis,…
Pulmonary hypertension describes a number of different diseases involving the pulmonary vasculature, which have haemodynamic, histological, and therapeutic features in common. The hallmark of these diseases is an abnormally high…
Even though, as stated by Lev and Eckner, 1 no two cases are exactly the same, it is the characteristic anatomy that permits the instant recognition of the tetralogy of…
Cardiac involvement in systemic disease can be broadly divided into those conditions in which the heart is involved in the disease process itself, and those in which a structural or…
In this chapter, we consider abnormalities of the pulmonary veins, in particular their anomalous connections to the systemic venous system. The variant of partially anomalous pulmonary venous connection associated with…
The essence of congenitally corrected transposition is the presence of discordant connections at both atrioventricular and ventriculo-arterial junctions. This segmental combination, like transposition itself (see Chapter 38 ), can be…
Common arterial trunk is a rare congenital malformation of the heart. As its name implies, its essential anatomical feature is the presence of an arterial trunk, which arises from the…
Abnormalities of the left ventricular outflow tract may occur at the subvalvar level, valvar, supravalvar, or a combination thereof. These abnormalities commonly co-exist with other left-sided lesions, such as aortic…
