Abstract: Biventricular repair requires two ventricles, each capable of supporting the systemic and pulmonary circulation. Septation has been interpreted as the pursuit of biventricular circulation rather than single-ventricle track. Although…
Abstract Double-outlet right ventricle (DORV) describes a ventriculoarterial connection in which both great arteries associate primarily with the right ventricle in an array of possible arrangements that can produce physiologies…
Abstract This chapter describes the disease spectrum of pulmonary atresia with intact ventricular septum (PA/IVS). It reviews the embryology, anatomy, physiology, treatment algorithms, and surgical techniques and outcomes. PA/IVS is…
Abstract Isomerism is a unique clinical entity in which there is duplication of one half of the body across the vertical axis, leading to a loss of laterality in the…
Abstract This chapter focuses on the indications and treatment options of pulmonary valve replacement. Currently there are multiple options for pulmonary valve replacement. However, there is no “perfect” valve for…
Abstract Pulmonary embolism (PE) is an uncommon but potentially fatal complication of venous thromboembolism (VTE). Congenital heart disease predisposes children to both VTE and, by association, PE. This is due…
Abstract This chapter focuses on the medical and surgical management of coronary artery anomalies in the pediatric patient without other congenital heart defects. The vast majority of aberrant coronary arteries…
Abstract Despite the advances in therapies and updated guidelines, infective endocarditis remains a cause of considerable morbidity and mortality in children. Infective endocarditis (IE) is defined as an infection of…
Abstract The population of adults with congenital heart disease is large and growing. This group has a high rate of health resource utilization, including hospital admissions. It is predicted that…
Abstract Transposition of the great arteries (d-TGA) occurs in 3 per 10,000 live births and makes up 5% to 7% of all congenital heart disease. Without surgery, less than 10%…
