Kawasaki Disease

Feb 26, 2019 by in CARDIOLOGY Comments Off on Kawasaki Disease

Definition/Morphology Tomisaku Kawasaki first reported Kawasaki disease (KD) in 1967. At first, KD was thought to be an acute and self-limiting febrile disorder; however, the first nationwide survey in Japan…

read more

Heterotaxy and Isomerism of the Atrial Appendages

Feb 26, 2019 by in CARDIOLOGY Comments Off on Heterotaxy and Isomerism of the Atrial Appendages

Definitions The term heterotaxy comes from the Greek heteros, meaning “other” and taxis, meaning “arrangement.” The nomenclature and definition of heterotaxy have been a matter of debate for years and…

read more

Atrioventricular Valve Atresia

Feb 26, 2019 by in CARDIOLOGY Comments Off on Atrioventricular Valve Atresia

In hearts with a univentricular atrioventricular connection both atria are connected to a single ventricle; this includes hearts with either atrioventricular valve (AVV) atresia or a double-inlet atrioventricular connection. Either…

read more

Transposition of the Great Arteries

Feb 26, 2019 by in CARDIOLOGY Comments Off on Transposition of the Great Arteries

Definition and Morphology The term transposition of the great arteries (TGA) describes the anatomic arrangement in which the aorta arises from the right ventricle (RV) and the pulmonary artery from…

read more

Eisenmenger Syndrome

Feb 26, 2019 by in CARDIOLOGY Comments Off on Eisenmenger Syndrome

Definition and Morphology In 1897, Victor Eisenmenger, an Austrian physician, first described both the clinical and pathologic features of irreversible pulmonary vascular disease in a 32-year-old man with a nonrestrictive…

read more

Double-Outlet Right Ventricle

Feb 26, 2019 by in CARDIOLOGY Comments Off on Double-Outlet Right Ventricle

Double-outlet right ventricle (DORV) is a “disease” that includes a family of anatomically related complex congenital heart lesions involving the right ventricular outflow tract (RVOT). There are several variations within…

read more

Tetralogy of Fallot

Feb 26, 2019 by in CARDIOLOGY Comments Off on Tetralogy of Fallot

Definition and Morphology It was Etienne-Louis Arthur Fallot who, in a series of papers in 1888, separated the malformation we now describe with his name from other anatomic lesions responsible…

read more

Pulmonary Atresia With Intact Ventricular Septum

Feb 26, 2019 by in CARDIOLOGY Comments Off on Pulmonary Atresia With Intact Ventricular Septum

Definition and Morphology Pulmonary atresia with intact ventricular septum (PAIVS) was first described by John Hunter in 1783. It is a rare congenital cardiac malformation with considerable morphologic heterogeneity, and…

read more

Double-Inlet Ventricle

Feb 26, 2019 by in CARDIOLOGY Comments Off on Double-Inlet Ventricle

Definition and Morphology The nomenclature for single ventricle has been a subject of debate for years. Double-inlet ventricle is commonly defined as the morphologic arrangement in which more than 50%…

read more
Premium Wordpress Themes by UFO Themes