Diagnosis
Age at imaging study (years)
Weight at study (kg)
Reason for printing
Modality
Did 3D model add value over prior imaging?
Pre-intervention cases: Did the 3D model aid in making management decisions?
Bicuspid aortic valve, severe dilation of aortic root and ascending aorta, moderate AR, dilated LV, mild LV dysfunction
20
83
Patient counseling
Trainee education
CT
Yes
N/A
Coarctation of aorta, s/p repair
21
55
Trainee education
MRI
No
N/A
DORV, s/p VSD closure (Rastelli) and RV-PA conduit. Complex LVOT obstruction
30
121
Pre-intervention planning
Patient counseling
Trainee education
MRI
Yes
Yes
Dextrocardia, DORV, right-sided IVC, extracardiac Fontan baffle to LPA, left SVC to left-sided superior cavo-pulmonary connection
31
64
Patient counseling
Trainee education
MRI
Yes
N/A
D-transposition of the great arteries, s/p atrial switch (Senning)
36
86
Patient counseling
Trainee education
MRI
Yes
N/A
DORV, D-malposition of the great arteries. H/o Blalock-Hanlon procedure (atrial septectomy), PA band in infancy. Followed by classic Glenn (SVC to RPA anastomosis), PA band takedown and modified Mustard procedure (IVC baffled to left atrium). Cyanosis and atrial arrhythmia
40
54
Pre-intervention planning
Patient counseling
Trainee education
MRI
Yes
Yes
DORV, s/p repair followed by RVOT reconstruction, SubAS resection. Recurrent LVOT obstruction
45
65
Pre-intervention planning
Patient counseling
Trainee education
MRI
Yes
Yes
Unbalanced AV canal, left dominant, superior-inferior atria, DORV, Taussig bing type, L-malposed great arteries, sub-PS, PS. Increasing cyanosis
45
67
Pre-intervention planning
Patient counseling
Trainee education
MRI
Yes
Yes
The following cases show specific applications of 3D printing in ACHD patients.
Case 1
A twenty-nine-year-old (121 kg) male with history of double outlet right ventricle (DORV) underwent a two ventricle repair with a Rastelli procedure, ventricular septal defect (VSD) closure with baffling of left ventricle (LV) to aorta, and RV to pulmonary artery (PA) conduit placement in early life. He presented with exercise intolerance. Cardiac MRI showed complex LVOT obstruction, a small residual VSD, dilation of aortic root (sinus of Valsalva), and aortic regurgitation. A 3D model was printed to aid in surgical planning. Figure 11.1 shows complex obstruction under the aortic valve with muscle bundles in the LVOT. Note the small VSD and buckling of the VSD patch into the LVOT. A catheter crosses the VSD from the RV with the tip in the LV. A ridge of muscle crosses the LVOT. Figure 11.1b shows a second model, created to simulate the “surgeon’s view.” Corresponding anatomy from the operating room is shown in Fig. 11.1c.
Fig. 11.1
a Complex obstruction under the aortic valve with muscle bundles in the LVOT. Note the small VSD and buckling of the VSD patch into the LVOT. A catheter crosses the VSD from the RV with the tip in the LV. A ridge of muscle crosses the LVOT. b Shows a second model, created to simulate the “surgeon’s view.” Corresponding anatomy from the operating room is shown in (c)
Case 2
A sixteen-year-old male with history of heterotaxy syndrome, single ventricle anatomy with a systemic RV, had undergone a total cavo-pulmonary connection (aka Fontan) palliation with an extracardiac fenestrated conduit. He subsequently underwent percutaneous device closure of the Fontan fenestration. A surveillance MRI was performed to evaluate single ventricle anatomy and physiology. A 3D model was printed for teaching purposes. The model (Fig. 11.2) shows a dilated and hypertrophied RV, the aorta as the only outflow from the functional single ventricle and the Fontan conduit and superior vena cava connecting to the pulmonary arteries. The fenestration occlusion device is shown in green.
Fig. 11.2
Dilated and hypertrophied RV, the aorta as the only outflow from the functional single ventricle and the Fontan conduit and superior vena cava connecting to the pulmonary arteries. The fenestration occlusion device is shown in green