Pectus Carinatum



Fig. 4.1
(a) Chondrogladiolar repair ; (b) mixed deformity repair; (c) chondromanubrial repair (From Chondrogladiolar.) [2]



Outcomes following the modified Ravitch repair for pectus carinatum are fairly positive with high postoperative patient satisfaction rates [25] and minimal complications. Complications reported include seroma, wound infection, pleural effusions, pneumothorax, and local tissue necrosis [1, 26]. Recurrence rates are reported to be 1.8–5.5 % [23, 24, 27]. Most authors advocate for delaying repair until after puberty in order to reduce the rate of recurrence [28].

The first minimally invasive technique for pectus carinatum repair was described in 1997 by Kobayashi et al. using a subcutaneous endoscopic technique with multiple stab incisions to facilitate the cartilage resection [29]. Other techniques described in the literature include using subpectoral insufflation or thoracoscopic-assisted methods to assist with rib resection [30, 31]. These techniques involve novel minimally invasive methods of creating operative space to perform the rib resection; however, widespread use is yet to be adopted.

In 2009, Abramson et al. described a novel technique not requiring cartilage resection to treat pectus carinatum in which a curved steel bar is inserted subcutaneously and fixed to the lateral ribs using fixation plates and subperiosteal wires. The bar applies manual pressure to the anterior chest wall until the desired anatomical configuration is achieved. In their initial series of 40 patients, “highly satisfactory results” were reported with 10/20 patients followed. Complications with this technique reported included pneumothorax requiring chest tube, skin adherence to the bar, seroma formation, wire malfunction, persistent pain, and wound infection. Based on the initial data, the study concluded that the best results could be seen in younger patients whose chest wall was more flexible [32]. It is also important to note that this bar-based technique is not useful in treating chondromanubrial defects where point of maximum protrusion is too superiorly located and there is more limited chest wall compliance.



Nonoperative Repair


Orthotic bracing was first described in Brazil to treat pectus carinatum in 1992 [33]. Bracing applies continuous direct pressure and counter-pressure over an extended period of time to the deformity enabling long-term remodeling of the costal cartilage. Patients with a compliant chest wall are most responsive to this treatment; thus, the best candidates have been those who are prepubertal between ages 10 and 15 [34]. A variety of bracing devices and protocols have evolved since the initial report in 1992 with complete resolution with the bracing alone to be between 65 and 80 % [15, 3539].

Regardless of brace type and protocol, the main determinant of success is patient compliance, and thus much of recent research efforts have focused primarily on manufacturing braces that are more comfortable, easily concealed, and with trackable usage [4043]. Outcomes following orthotic bracing are fairly positive with excellent patient satisfaction and efficacy [44]. Recurrence rates after removal of the brace range between 5 and 15 % [34, 35]. Complications are generally minor and include skin changes, back pain, and hematoma. Of note, case reports of overcorrection to an iatrogenic excavatum have been reported [45]; thus, close follow-up of these patients is required. At many centers, bracing is now considered the first option for intervention offered in patients with chondrogladiolar deformities [46].


References



1.

Shamberger RC, Welch KJ. Surgical correction of pectus carinatum. J Pediatr Surg. 1987;22(1):48–53.CrossRefPubMed


2.

Kelly Jr RE, Shamberger RC. Chapter 62—congenital chest wall deformities. In: Coran AG, editor. Pediatric surgery. 7th edn. Philadelphia: Mosby; 2012. p. 779–808. http://​dx.​doi.​org/​10.​1016/​B978-0-323-07255-7.​00062-3


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Fonkalsrud EW. Pectus carinatum: the undertreated chest malformation. Asian J Surg. 2003;26(4):189–92. doi:10.​1016/​S1015-9584(09)60300-6.CrossRefPubMed


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Lopushinsky SR, Fecteau AH. Pectus deformities: a review of open surgery in the modern era. Semin Pediatr Surg. 2008;17(3):201–8. http://​dx.​doi.​org/​10.​1053/​j.​sempedsurg.​2008.​03.​009


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Desmarais TJ, Keller MS. Pectus carinatum. Curr Opin Pediatr. 2013;25(3):375–81. doi:10.​1097/​MOP.​0b013e3283604088​.CrossRefPubMed


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Papadakis K, Shamberger RC. Congenital chest wall deformities. In: Sellke FW, Del Nido PJ, Swanson SJ, editors. Sabiston & Spencer surgery of the chest. 9th ed. Philadelphia: Elsevier; 2016. p. 399–429.


7.

Brodkin HA. Congenital chondrosternal prominence (pigeon breast) a new interpretation. Pediatrics. 1949;3(3):286–95.PubMed


8.

Robicsek F, Cook JW, Daugherty HK, Selle JG. Pectus carinatum. Coll Works Cardiopulm Dis. 1979;22:65–78.PubMed


9.

Welch KJ, Vos A. Surgical correction of pectus carinatum (pigeon breast). J Pediatr Surg. 1973;8(5):659–67.CrossRefPubMed


10.

Currarino G, Silverman FN. Premature obliteration of the sternal sutures and pigeon-breast deformity. Radiology. 1958;70(4):532–40. doi:10.​1148/​70.​4.​532.CrossRefPubMed


11.

Ravitch MM. Unusual sternal deformity with cardiac symptoms operative correction. J Thorac Surg. 1952;23(2):138–44.PubMed

Apr 25, 2017 | Posted by in CARDIAC SURGERY | Comments Off on Pectus Carinatum

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