PP-152 Congenital Cardiac Malformations in Turner Syndrome




Aim


To describe the spectrum and frequency of cardiovascular abnormalities in pediatric and young adult patients with Turner Syndrome (TS) using cardiac MRI, MR angiography and transthoracic echocardiography(TTE).




Methods


This prospective study consisted of 47 female patients of the pediatric age and young adults with a karyotypically confirmed diagnosis of TS. All patients underwent cardiac MRI and contrast-enhanced MR angiography. A second examination after 9-26 months was performed in 28 of these patients. In 18 cases TTE concurrent with the MRI assessment were done.




Results


Elongation of the transverse aortic arch (ETA) was the most frequent abnormality with a rate of 37%. The rate of partial anomalous pulmonary venous connection was 21.7%, bicuspid aortic valve (BAV) was 19.6%, and coarctation was 6.5%. The rate of the ascending aorta dilatation was 28.3% and the descending aorta dilatation was 15.2%. The diameters of the aorta and the rate of aortic dilatation per unit time was greater in the patients with BAV (p<0.05). ETA was less observed in the patients who were receiving growth hormone (GH) therapy (p<0.05).

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Nov 30, 2016 | Posted by in CARDIOLOGY | Comments Off on PP-152 Congenital Cardiac Malformations in Turner Syndrome

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