Objective
Pulmonary arterial hypertension (PAH) is hemodynamically pathophysiological condition defined as increase of secondary pulmonary arterial pressure, at rest over 25, or after effort over 30 mmHg, measured by right heart catheterization. In everyday pediatric clinical practice, common problem is the estimation of PAH associated with congenital heart defects (CHD), where the increase in pulmonary vascular resistance leads to irreversible changes in pulmonary vasculature (Eisenmenger’s syndrome), which is a contraindication for surgical treatment. The treatment of PAH is full of contradictions, uncertainty and inexperience. The aim of this study was to point out the problem, to show the importance of early diagnosis, assessment and treatment of PAH associated with CHD.
Methods
The study included data of registered patients with PAH associated with CHD from PAH register and protocols of catheterized children (311 catheterizations, 63.75% diagnostic) from the period May 1998. -January 2015. in the Clinical Center University of Sarajevo.
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