Objective
Pulmonary atresia with intact ventricular septum is a rare anomaly of the Congenital Heart Diseases(CHD). It is seen aproximately in 3% of all CHDs. Management strateggies may vary. Patients clinical status, the development stage of right ventricle, tricuspit valve and right ventricle dependent coronary arterial circulation are the most important criteria of choosing the treatment modality. Transcatheteric and urgent surgical approaches play an important role as the life-saving procedures. The aim of this study is evaluate to characteristics of our patients who underwent percutaneous procedures and the results of processes.
Methods
Electrocardiography, chest radiograph, echocardiography and angiography was performed in all patients. The echocardiographic recordings at the time of diagnosis were collected to determine type of atresia(membraneus or muscular), right ventricle size and morphology, tricuspit valve Z score, degree of tricuspit regurgitation, coronary artery abnormalities and ductal shunt. Angiographic data were taken from angiography based registry system. Hemodynamic data were compared before and after treatment for patients atretic valve perforation.
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