A full-term female newborn with prenatal diagnosis of ventricular asymmetry was referred to our department for postnatal echocardiographic evaluation. Two-dimensional echocardiography revealed a coarctation of the aorta ( Fig. 1 A ), a bicuspid aortic valve ( Fig. 1 B) and a double-orifice mitral valve (DOMV) ( Fig. 2 A, Video 1 ). Three-dimensional echocardiography showed two distinct orifices of unequal size divided by a complete fibrous bridge ( Fig. 2 B). The smaller orifice was situated laterally ( Fig. 2 A and B). There was no mitral stenosis or insufficiency. The mitral annulus was of normal size and two papillary muscles were clearly distinguished. Surgical repair of the mitral valve was not performed. The coarctation of the aorta was treated surgically at day 7 with the conventional technique of resection and end-to-end anastomosis (Crafoord’s operation). The postoperative course was uneventful.
