Bicuspid aortic valve is a common congenital heart defect.

Aim .– Point out the importance of bicuspid aortic valve in children, and the importance of monitoring these children.

Patients .– We examined by echocardiography 1830 children: 2 months of age to 18 years old −978 (53.44%) boys and 852 (46.56%) girls for heart murmur or symptoms of the cardiovascular system. Study was carried out using Siemens Sonoline G50. Measurements are performed in 2D and M-mode. Echocardiographic diagnosis of these defects is based on the existence of two aortic cusps, instead of normal three, often asymmetrical, with one line of coaptation consisting of both commissure.

Results .– Among the children examined, 15 (0.82%) children were with bicuspid aortic valve, 11 (1.12%) boys and four (0.47%) girls. Frequency was higher in boys.

There were two boys with bicuspid aortic valve, one with aortic stenosis, two with aortic insufficiency, six children (five boys and one girl) with aortic stenosis and regurgitation. Four children (one boy and three girls) had aortic coarctation.

Monitoring the children in 4-year period, three children deteriorated aortic stenosis. In one boy there was no aortic regurgitation, but after a year, it appeared. Enlarged area of the sinus Valsalva was registered in one boy.

Conclusion .– It is important to monitor children with bicuspid aortic valves, because these children are at increased risk of complications including aortic valvular disease, ascending aorta aneurysm and aortic dissection. Patients with bicuspid aortic valve are also at higher risk of aortic coarctation.